Batten disease (JNCL) is linked to disturbances in mitochondrial, cytoskeletal, and synaptic compartments

Kaisu Marjaana Luiro, Outi Kopra, Jan Tomas Blom, Massimiliano Gentile, Hannah Mitchison, Iiris Hovatta, Kid Törnquist, Anu Jalanko

Research output: Contribution to journalArticleScientificpeer-review

Original languageEnglish
JournalJournal of Neuroscience Research
Volume84
Issue number5
Pages (from-to)1124-1138
Number of pages15
ISSN0360-4012
DOIs
Publication statusPublished - 2006
MoE publication typeA1 Journal article-refereed

Fields of Science

  • CLN3
  • lysosomal
  • neurodegenerative disease
  • mitochondria
  • cytoskeleton
  • synaptosome
  • NEURONAL CEROID-LIPOFUSCINOSIS
  • MOUSE MODEL
  • CYTOPLASMIC DYNEIN
  • AXONAL-TRANSPORT
  • GENE-EXPRESSION
  • ATP-SYNTHASE
  • DYNACTIN COMPLEX
  • LATE-INFANTILE
  • CLN3 PROTEIN
  • SUBUNIT

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