Palmitoyl protein thioesterase 1 (Ppt1)-deficient mouse neurons show alterations in cholesterol metabolism and calcium homeostasis prior to synaptic dysfunction

Laura Ahtiainen, Julia Kolikova, Aino-Liisa Mutka, Kaisu Luiro, Massimiliano Gentile, Elina Ikonen, Leonard Khiroug, Anu Jalanko, Outi Kopra

Research output: Contribution to journalArticleScientificpeer-review

Original languageEnglish
JournalNeurobiology of Disease
Volume28
Pages (from-to)52-64
Number of pages13
ISSN0969-9961
DOIs
Publication statusPublished - 2007
MoE publication typeA1 Journal article-refereed

Fields of Science

  • palmitoyl protein thioesterase 1
  • infantile neuronal ceroid lipofuscinosis
  • neuron culture
  • synapse
  • neuron maturation
  • calcium homeostasis
  • cholesterol
  • microarray
  • CEROID-LIPOFUSCINOSIS
  • ALPHA-SYNUCLEIN
  • ALZHEIMERS-DISEASE
  • GLIAL ACTIVATION
  • BATTEN-DISEASE
  • GENE ONTOLOGY
  • KNOCKOUT MICE
  • BRAIN-SLICES
  • INFANTILE
  • NEURODEGENERATION
  • 118 Biological sciences
  • 311 Basic medicine
  • 515 Psychology

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