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The Neuronal Ceroid Lipofuscinosis Protein CLN5: New Insights into Cellular Maturation, Transport, and Consequences of Mutations

  • Mia-Lisa Schmiedt
  • , Carlos Bessa
  • , Claudia Heine
  • , Maria Gil Ribeiro
  • , Anu Jalanko
  • , Aija Kyttälä

Research output: Contribution to journalArticleScientificpeer-review

Original languageEnglish
JournalHuman mutation
Volume31
Issue number3
Pages (from-to)356-365
Number of pages10
ISSN1059-7794
DOIs
Publication statusPublished - 2010
MoE publication typeA1 Journal article-refereed

Fields of Science

  • Neuronal ceroid lipofuscinoses
  • NCL
  • CLN5
  • lysosomal trafficking
  • protein N-glycosylation
  • LYSOSOMAL PROTEINS
  • BATTEN-DISEASE
  • IDENTIFICATION
  • RECEPTORS
  • SITES
  • 312 Clinical medicine

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